Prasse, AntjeAntjePrasse2023-07-062023-07-062016https://publica.fraunhofer.de/handle/publica/44523410.1183/2312508X.10005615This chapter summarises recent advances regarding definition, clinical features, underlying mechanisms, and management of acute exacerbation of IPF. Whilst recent studies suggest risk modulation for acute exacerbations may become feasible with treatment, shortcomings in the current definition and a need for standardised diagnostic algorithms have become apparent.enbook article